%0 Journal Article
%T 进展性肺纤维化病例报告1例及文献复习
A Case of Progressive Pulmonary Fibrosis and Literature Review
%A 马舒婷
%A 刘耀
%A 陈云凤
%A 蔡雨芹
%J Journal of Clinical Personalized Medicine
%P 1-5
%@ 2334-3443
%D 2025
%I Hans Publishing
%R 10.12677/jcpm.2025.42138
%X 进展性肺纤维化(progressive pulmonary fibrosis, PPF)是一类表现为肺纤维化程度进行性加重、肺生理功能下降导致患者早期死亡的非特发性肺纤维化(idiopathic pulmonary fibrosis, IPF)的疾病的统称,其病情进展迅速,治疗难度大,预后差。结缔组织相关间质性肺病(interstitial lung disease associated with connective tissue disease, CTD-ILD)是PPF重要的分型。侵袭性肺曲霉菌病(Invasive pulmonary aspergillosis, IPA)具有高致死率的特点,其发病呈逐年增长趋势。本文报道1例进展性肺纤维化合并侵袭性肺曲霉菌感染典型病例,总结其诊治要点,以相关文献复习。
PPF includes non-idiopathic pulmonary fibrosis that aggravates progressively pulmonary fibrosis and lung function causing early death and presents rapid progress, difficult treatment, and poor prognosis. CTD-ILD is important for this. IPA presents high fatality rate and incidence increase. It reports a case of PPF combined with IPA, summarizes diagnosis and treatment, and reviews relevant literature.
%K 进展性肺纤维化,
%K 侵袭性肺曲霉菌病,
%K 结缔组织相关性间质性肺病
Progressive Pulmonary Fibrosis
%K Invasive Pulmonary Aspergillosis
%K Connective Tissue-Associated Interstitial Lung Disease
%U http://www.hanspub.org/journal/PaperInformation.aspx?PaperID=108518