%0 Journal Article %T Profound hypernatremia due to central diabetes insipidus in a child with lobar holoprosencephaly %J Jaffna Medical Journal %D 2018 %R 10.4038/jmj.v30i2.24 %X This case report presents a rare endocrine disorder highlights the significance of serum electrolyte measurement in children with congenital brain abnormalities presenting with convulsion. It also emphasizes the importance of careful urine volume estimation in diapered infants suspected to have polyuria %K Central Diabetes Insipidus %K Polyuria hypernatremia %U https://jmj.sljol.info/articles/10.4038/jmj.v30i2.24/