%0 Journal Article
%T A case of ruptured sinus of Valsalva aneurysm and reversible flow
%A Basil Al-Sabeq
%A Ryan Davey
%A Sabe De
%J Pulmonary Circulation
%@ 2045-8940
%D 2018
%R 10.1177/2045894018760656
%X Pulmonary hypertension (PH) in adults with congenital heart disease (CHD) and significant systemic-to-pulmonary shunting is a significant cause of morbidity and mortality. Its pathophysiology is incompletely understood, but involves a flow-induced pulmonary arteriopathy characterized by endothelial cell dysfunction and vascular remodeling that alters pulmonary arterial vasoreactivity. There is a paucity of literature linking PH with left-to-right shunting due to ruptured sinus of Valsalva aneurysms (SOVA). We present a unique case of reversible, flow-associated PH due to a ruptured congenital right SOVA fistulizing into the right atrium (RA), with emphasis on non-invasive and invasive assessment of pulmonary hemodynamics before and after surgical intervention
%K congenital
%K echocardiography
%K right atrium
%K shunt
%U https://journals.sagepub.com/doi/full/10.1177/2045894018760656