%0 Journal Article
%T Primary pulmonary angiosarcoma: case reports and review of the literature
%A Chitra Viswanathan
%A Mayur Virarkar
%A Priya Bhosale
%A Rajesh Thampy
%A Sidra Tayyab
%J Asian Cardiovascular and Thoracic Annals
%@ 1816-5370
%D 2019
%R 10.1177/0218492319836910
%X Pulmonary artery angiosarcoma is a rare malignant vascular tumor with an aggressive clinical course and a poor prognosis. Hemoptysis and shortness of breath have been reported as common clinical presentations. The exact clinicopathology is unknown. A tissue specimen obtained by percutaneous fine-needle aspiration cytology or open/thoracoscopic biopsy can confirm the diagnosis based on histopathological and immunohistochemical features. The differential diagnosis includes pulmonary thromboembolism, vascular malformations, and lung carcinoma. There is a paucity of literature describing this tumor, with only a few case reports available. There is also a lack of standardized guidelines for management, which further worsens the survival outcome. We report 3 cases of pulmonary artery angiosarcoma and review the recent literature
%K Diagnosis
%K differential
%K hemangiosarcoma
%K immunohistochemistry
%K mediastinal neoplasms
%K pulmonary artery
%K vascular neoplasms
%U https://journals.sagepub.com/doi/full/10.1177/0218492319836910