%0 Journal Article
%T A case of periampullary adenocarcinoma in neurofibromatosis type 1
%A Ali A. Siddiqui
%A Ashwin R. Sama
%A C. Andrew Kistler
%A Jeffrey P. Baliff
%A Jennifer M. Johnson
%A Jordan M. Winter
%J SCIE-indexed Journal
%D 2014
%X Neurofibromatosis type 1 (NF-1), also known as von Recklinghausen¡¯s disease, is an autosomal-dominant disorder affecting males and females equally with an incidence of approximately one in 3,000 births (1,2). The classic clinical findings include caf¨¦-au-lait spots, cutaneous neurofibromas, cognitive impairment, axillary and/or inguinal freckling, Lisch nodules (pigmented hamartomatous nevus of the iris) and bony abnormalities. In addition to these findings, patients with NF-1 also have an increased incidence of both benign and malignant neoplasms with the most common sites including the nervous system, skin, muscles and gastrointestinal tract
%U http://jgo.amegroups.com/article/view/2855/html