%0 Journal Article %T An unusual presentation of purine nucleoside phosphorylase deficiency mimicking systemic juvenile idiopathic arthritis complicated by macrophage activation syndrome %A Alessia Arduini %A Antonella Insalaco %A Claudia Bracaglia %A Emiliano Marasco %A Fabrizio De Benedetti %A Gian Marco Moneta %A Giulia Marucci %A Giusi Prencipe %A Ivan Caiello %A Manuela Pardeo %J Archive of "Pediatric Rheumatology Online Journal". %D 2019 %R 10.1186/s12969-019-0328-3 %X Laboratory parameters and cytokine levels during disease cours %K Macrophage activation syndrome %K Juvenile idiopathic arthritis %K Interferons %K Interleukins %K Chemokines %U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6532153/