%0 Journal Article
%T Original research article: Association and diagnostic utility of diastolic dysfunction and myocardial fibrosis in patients with Fabry disease
%A Christoph Wanner
%A Dan Liu
%A Daniel Oder
%A Frank Weidemann
%A Georg Ertl
%A Jonas M¨¹ntze
%A Kai Hu
%A Peter Nordbeck
%A Sebastian Herrmann
%A Stefan Frantz
%A Stefan St£¿rk
%A Tim Salinger
%J Archive of "Open Heart".
%D 2018
%R 10.1136/openhrt-2018-000803
%X Current guidelines highlight important therapy implications of cardiac fibrosis in patients with Fabry disease (FD). However, association between morphological and functional impairments with cardiac fibrosis in hereditary cardiomyopathies remains elusive. We investigated the association between echocardiography-determined cardiac dysfunction and cardiac MRI (cMRI)-detected myocardial fibrosis (late gadolinium enhancement, LE) in patients with FD with preserved left ventricular ejection fraction (¡Ý50%)
%K echocardiography
%K Fabry
%K MRI
%U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6045729/