%0 Journal Article
%T Porokeratotic eccrine and hair follicle nevus: a report of two cases
and review of the literature
%A Alfredo Daniel Agull¨®-P¨¦rez
%A Alicia C¨®rdoba-Iturriagagoitia
%A Juan Ignacio Yanguas-Bayona
%A Miguel ¨˘ngel Resano-Abarzuza
%J Archive of "Anais Brasileiros de Dermatologia".
%D 2017
%R 10.1590/abd1806-4841.20176536
%X Porokeratotic eccrine and hair follicle nevus is a very rare non-hereditary disorder of keratinization with eccrine and hair follicle involvement with only 9 cases described in the literature. In 2009 the term porokeratotic anexial ostial nevus was proposed to comprehend porokeratotic eccrine and hair follicle nevus and a related and more common process without follicular involvement: porokeratotic eccrine ostial and dermal duct nevus Recent findings suggest that both entities may be produced by a mutation in GJB2 gene, which is associated to KID syndrome. Herein we report 2 cases of porokeratotic eccrine and hair follicle nevus and review the existing cases in the Spanish and English literature
%K Hamartoma
%K Keratinocytes
%K Nevus
%K Pediatrics
%U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5726699/