%0 Journal Article %T A rare case of Erdheim-Chester disease in the breast %A Aboelkhair M. Al-gahmi %A Elham Rawah %A Razan F. Binyousef %A Zahid Rahman Khan %J Archive of "Annals of Saudi Medicine". %D 2017 %R 10.5144/0256-4947.2017.79 %X Erdheim-Chester disease (ECD) is rare non-Langerhans histiocytosis with distinctive radiologic and pathologic entities. We report a rare case of which ECD was involving the breast with only eight similar cases reported in the English literature. Our patient was a 52-year-old female patient with ECD involving the breast, mesentery, left kidney, retroperitoneum and the skeleton. The diagnosis was based on distinctive imaging and histopathological findings. The patient received a new novel treatment as part of a clinical trial in the United States and showed clinical and radiological improvement %U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6148982/