%0 Journal Article %T Efficacy and safety of an intravenous C1-inhibitor concentrate for long-term prophylaxis in hereditary angioedema %A Arthur Vegh %A Debora Williams-Herman %A Henrike Feuersenger %A Inmaculada Martinez-Saguer %A James W. Baker %A Jonathan A. Bernstein %A Jonathan Edelman %A Marc A. Riedl %A Markus Magerl %A Mikhail Rojavin %A Paula Busse %A Ralph Shapiro %A Thomas Machnig %A Timothy Craig %A William Lumry %J Archive of "Allergy & Rhinology". %D 2017 %R 10.2500/ar.2017.8.0192 %X The plasma-derived, pasteurized, nanofiltered C1-inhibitor concentrate (pnfC1-INH) is approved in the United States as an intravenous (IV) on-demand treatment for hereditary angioedema (HAE) attacks, and, in Europe, as on demand and short-term prophylaxis %K Berinert %K hereditary angioedema %K long-term prophylaxis %K plasma-derived C1-inhibitor %K registry %K safety %K efficacy %K thromboembolic events %K self-administration %K dosing %U https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5380447/