%0 Journal Article
%T Idiopathic Macular Telangiectasia Associated With Large Soft Drusen and Retinal Angiomatous Proliferation - Idiopathic Macular Telangiectasia Associated With Large Soft Drusen and Retinal Angiomatous Proliferation - Open Access Pub
%A Claudio Campa
%A Perri Paolo
%J OAP | Home | Journal of Ophthalmic Science | Open Access Pub
%D 2018
%X Idiopathic macular telangiectasia type 2 is a rare retinal condition usually characterized by parafoveal telangiectatic vessels, hyperplastic pigment plaques and seldom a full thickness macular hole or a retinal neovascularisation. Herein we describe an atypical presentation of this disease. Methods Review of the patient¡¯s clinical and angiographic records. Results A 87-year-old white man was diagnosed with idiopathic macular telangectasia type 2. Ophthalmological and angiographic examination disclosed telangiectasia of the parafoveal capillaries together with extensive bilateral granular soft drusen and unilateral retinal angiomatous proliferation (RAP). Initially photodynamic therapy with verteporfin (PDT) and subsequently intravitreal injections of bevacizumab were used to treat RAP lesion. This approach provided visual acuity stabilization up to 24 months. Conclusion This case of ours shows that drusen may be a feature of macular teleangiectasia type 2. It also emphasizes that PDT and anti-VEGF therapy are both safe and effective for treating neovascular complications of this disease. Review of the patient¡¯s clinical and angiographic records. A 87-year-old white man was diagnosed with idiopathic macular telangectasia type 2. Ophthalmological and angiographic examination disclosed telangiectasia of the parafoveal capillaries together with extensive bilateral granular soft drusen and unilateral retinal angiomatous proliferation (RAP). Initially photodynamic therapy with verteporfin (PDT) and subsequently intravitreal injections of bevacizumab were used to treat RAP lesion. This approach provided visual acuity stabilization up to 24 months. This case of ours shows that drusen may be a feature of macular teleangiectasia type 2. It also emphasizes that PDT and anti-VEGF therapy are both safe and effective for treating neovascular complications of this disease. DOI 10.14302/issn.2470-0436.jos-15-710 Macular telangiectasia type 2 is a retinal vascular disorder characterized by crystalline intra-retinal deposits in the early stages and telangiectatic vessels and hyperplastic pigment plaques in advanced stages. Herein we describe an atypical presentation of the disease, with bilateral drusen and a neovascular lesion resembling a retinal angiomatous proliferation. Idiopathic juxtafoveolar retinal telangiectasis (IJT) was a term proposed by Gass and Oyakawa1 to describe a retinal vascular disorder characterized by dilated retinal capillaries around the foveal avascular zone without any known cause in contrast to secondary telangiectasia, for example,
%U https://www.openaccesspub.org/jos/article/268