%0 Journal Article %T Successful Handling of Disseminated BCG Disease in a Child with Severe Combined Immunodeficiency %A S¨Ēlvia Bacalhau %A Cristina Freitas %A Rosalina Valente %A Deolinda Barata %A Concei o Neves %A Katrin Sch fer %A Annelie Lubatschofski %A Ansgar Schulz %A Jo o Farela Neves %J Case Reports in Medicine %D 2011 %I Hindawi Publishing Corporation %R 10.1155/2011/527569 %X In high-burden countries, Mycobacterium bovis Bacillus Calmette-Guérin (BCG) vaccine is administered in newborn to prevent severe Mycobacterium tuberculosis infection. Because life-threatening disseminated BCG disease may occur in children with primary immunodeficiency, vaccination strategy against tuberculosis should be redefined in non-high-burden countries. We report the case of a patient with X-linked severe combined immunodeficiency (SCID) who developed disseminated BCG disease, highlighting the specific strategies adopted. %U http://www.hindawi.com/crim/medicine/2011/527569/