%0 Journal Article %T 热性感染相关性癫痫综合征1例报道
Febrile Infection-Related Epilepsy Syndrome: A Case Report %A 查剑 %A 易招师 %A 钟建民 %A 虞雄鹰 %A 吴华平 %A 陈勇 %J Asian Case Reports in Pediatrics %P 50-52 %@ 2328-0441 %D 2013 %I Hans Publishing %R 10.12677/ACRP.2013.13013 %X 目的:讨热性感染相关性癫痫综合征(febrile infection-related epilepsy syndrome, FIRES)的临床特点和诊疗对策。方法:对我院收治的1FIRES患儿的临床资料进行回顾性分析。结果:患儿以精神行为异常起病,起病前有发热感染病史,病程中出现难治性部分性癫痫持续状态(refractory partial status epilepticus, RPSE),经经验性抗中枢神经系统感染治疗及多种抗癫痫药物(antiepileptie drugs, AEDs)联合治疗2月,发作未控制,家属放弃治疗出院,出院后20天患儿死于癫痫持续状态(SE)结论FIRES临床中少见,目前治疗困难,应注意早期识别,尽早予以大剂量抗癫痫药物Febrile Infection-Related Epilepsy Syndrome %K Status Epilepticus %K Ketogenic Diet %U http://www.hanspub.org/journal/PaperInformation.aspx?PaperID=12181