%0 Journal Article %T Mckusick-Kaufman Syndrome Presenting as Acute Intestinal Obstruction %A Ramesh B Hatti %A Ashok V Badakali %A R N Vanaki %A VijayMahantesh S Samalad %J Journal of Neonatal Surgery %D 2013 %I EL-MED-Pub Publishers %X Hydrometrocolpos and polydactyly have been associated with many syndromes and can present at any age. Rarely does hydrometrocolpos present as neonatal intestinal obstruction. We report two cases of McKusick-Kaufman syndrome presenting with intestinal obstruction. In both cases, intestinal obstruction got relieved after a cutaneous vaginostomy. %K Hydrometrocolpos %K McKusick-Kaufman syndrome %K Neonatal intestinal obstruction %U http://www.jneonatalsurg.com/ojs/index.php/jns/article/view/23