%0 Journal Article
%T Synchronous multiple small bowel intussusceptions in an adult with blue rubber bleb naevus syndrome: Report of a case and review of literature
%A Clement Lee
%A Debasish Debnath
%A Tara Whitburn
%A Mark Farrugia
%A Federico Gonzalez
%J World Journal of Emergency Surgery
%D 2008
%I BioMed Central
%R 10.1186/1749-7922-3-3
%X We report the case of a 37-year-old man who presented with multiple intussusceptions of small bowel. He required an urgent laparotomy and bowel resections. He suffered from BRBNS. This is the first reported case of multiple synchronous intussusceptions affecting both jejunum and ileum, secondary to haemangiomas occurring in an adult with BRBNS. The underlying conditions of acute abdomen in patients with BRBNS may include intramural haemorrhage, infarction, volvulus or intussusception of bowel. Treatment options include pharmacological manipulation, bowel resection, and interventions such as sclerotherapy, angiographic embolisation, endoscopic ligation, electrocautery and laser photocoagulation for visceral lesions.A high index of suspicion is required whilst dealing with acute abdomen in patients with BRBNS. Clinical trials may provide some answers as to the preference of treatment in individual cases, as the current level of evidence does not offer a clear choice of optimal treatment.Management of acute abdomen in a patient suffering from blue rubber bleb naevus syndrome can be challenging. We report a unique case of intestinal intussusception in such a patient, who was treated successfully without any complication. We discuss relevant details and provide a review of literature. Optimal management of this condition remains unclear. We intend to make readers aware of potentially serious underlying conditions while dealing with acute abdomen in patients of blue rubber bleb naevus syndrome and highlight the need for optimising various treatment options.A 37-year-old male presented at Accident and Emergency department with chief complaints of colicky abdominal pain, nausea and vomiting of twelve hours' duration. The pain was generalised in nature, moderate in severity, and not associated with any aggravating or relieving factor. There was no alteration of bowel habit. His past medical history included multiple blood transfusions for 'anaemia' since childhood, Hepatitis
%U http://www.wjes.org/content/3/1/3