%0 Journal Article
%T Poroqueratosis de Mibelli. Presentaci¨®n de un caso familiar. Porokeratosis of Mibelli: a Family Case Report.
%A Rafael Pila P¨¦rez
%A Victor Adolfo Holgu¨ªn Prieto
%A Pedro Rosales Torres
%J MediSur
%D 2011
%I Centro Provincial de Informaci¨®n de las Ciencias M¨¦dicas en Cienfuegos
%X Se presenta el estudio de una familia portadora de poroqueratosis de Mibelli, entidad rara en nuestro medio. Se se alan los aspectos etiol¨®gicos, histopatol¨®gicos y cl¨ªnicos de esta enfermedad, con ¨¦nfasis en la profilaxis y el control de pacientes con este tipo de lesiones, ya que presentan un potencial neopl¨¢sico significativo. Se concluye que el conocimiento de esta enfermedad es necesario para varias ramas de la medicina: gen¨¦tica, dermatolog¨ªa, medicina interna, patolog¨ªa y oncolog¨ªa. The case study of a family carrying Porokeratosis of Mibelli is presented. This entity is very rare to be found in our country. Etiological, histopathological and clinical aspects are provided in this article. The importance of prophylaxis and monitoring of these patients is strongly emphasized due to the potential risk of malignancies they present. Finally, it has been concluded that knowledge on porokeratosis is essential to several medical specialities, such as genetics, dermatology, internal medicine, pathology and oncology.
%K Poroqueratosis
%K neoplasias cut¨¢neas
%K enfermedades cut¨¢neas gen¨¦ticas
%U http://www.medisur.sld.cu/index.php/medisur/article/view/1516