%0 Journal Article
%T Aneurismas de aorta abdominal e il¨ªaca y s¨ªndrome de Loeys- Dietz Abdominal aortic iliac aneurysms and Loeys-Dietz syndrome
%A David Ortiz Limonta
%A Dalia S¨¢nchez De la Guardia
%A Lilia Ch¨¦rcoles Cazate
%J MEDISAN
%D 2013
%I Centro Provincial de Ciencias M¨¦dicas
%X Se presenta el caso cl¨ªnico de una paciente de 29 a os de edad, con antecedentes de ectasia a¨®rtica, quien hab¨ªa sido estudiada a los 18 a os mediante cineangiograf¨ªa y se hall¨® un aneurisma fusiforme de la aorta abdominal infrarrenal y de la arteria il¨ªaca primitiva izquierda, de causa no precisada, las cuales fueron sustituidas con derivaci¨®n aortofemoral izquierda. Posteriormente, en el 2012, present¨® dolor y aumento del volumen en la regi¨®n inguinal izquierda, por lo que fue atendida en el Cuerpo de Guardia del Hospital Provincial Docente Clinicoquir¨²rgico "Saturnino Lora Torres" de Santiago de Cuba, y evaluada por especialistas del Servicio de Angiolog¨ªa y Cirug¨ªa Vascular, los cuales determinaron operarle de urgencia, al observar un aneurisma anastom¨®tico de la arteria femoral izquierda, de causa mic¨®tica, y las caracter¨ªsticas: craneosinostosis, ¨²vula b¨ªfida y hendidura del paladar; propias del s¨ªndrome de Loeys-Dietz The case report of a 29 year-old patient, with a history of aortic ectasia who had been studied when she was 18 years through cineangiography is presented and a fusiform aneurysm of the infrarrenal abdominal aorta and of the left primitive iliac artery, of unspecific cause was found, which were substituted with left aortofemoral bypass. Later on, in 2012, she presented pain and increase of the volume in the left inguinal region, reason why she was assisted in the emergency room of "Saturnino Lora Torres" Teaching Provincial Clinical Surgical Hospital in Santiago de Cuba, and evaluated by specialists of the Angiology and Vascular Surgery Service, which determined to treat her with an emergency surgery, when observing an anastomotic aneurysm of the left femoral artery of fungal cause, and the characteristics: craneosinostosis, bifid uvula and cleft palate; characteristic of Loeys Dietz syndrome.
%K s¨ªndrome de Loeys-Dietz
%K aneurisma de la aorta abdominal
%K aneurisma anastom¨®tico de la arteria femoral
%K derivaci¨®n aortofemoral izquierda
%K Servicio de Angiolog¨ªa y Cirug¨ªa Vascular
%K Loeys-Dietz syndrome
%K abdominal aorta aneurysm
%K anastomotic aneurysm of the femoral artery
%K left aortofemoral bypass
%K Angiology and Vascular Surgery Service
%U http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S1029-30192013000400019