%0 Journal Article %T Tumores neuroendocrinos gastrointestinales %A Daniel Z¨²£¿iga Monge %J Medicina Legal de Costa Rica %D 2013 %I Asociaci¨®n Costarricense de Medicina Forense %X Los tumores neuroendocrinos gastrointestinales (TNEG), tambi¨¦n llamados tumores carcinoides gastrointestinales, son neoplasias derivadas de c¨¦lulas neuroendocrinas. Pueden formarse en todo el sistema gastrointestinal, siendo el ¨ªleon el lugar de origen m¨¢s frecuente. Su forma de aparici¨®n es espor¨¢dica o asociada a s¨ªndromes familiares como von Hippel Lindau y neurofibromatosis. Los TNEG se diagnostican en su mayor¨ªa ya cuando la neoplasia ha invadido ganglios linf¨¢ticos u otros ¨®rganos distantes, ejemplo de esto es el s¨ªndrome carcinoide que se desarrolla por invasi¨®n hep¨¢tica tumoral. La cirug¨ªa es el ¨²nico tratamiento curativo. Gastrointestinal neuroendocrine tumors (TNEG), also called gastrointestinal carcinoid tumors, are neoplasms arising from neuroendocrine cells. They may form all around the gastrointestinal system, being the ileum the most common place of origin. Its form of onset is sporadic or associated with familial syndromes such as von Hippel Lindau and neurofibromatosis. TNEG are mostly diagnosed when the tumor has already invaded lymph nodes or distant organs, being an example of this the carcinoid syndrome; which develops as a manifestation of hepatic invasion. Surgery is the only curative treatment. %K Tumores neuroendocrinos gastrointestinales %K s¨ªndrome carcinoide %K cirug¨ªa. %K Gastrointestinal neuroendocrine tumors %K carcinoid syndrome %K surgery. %U http://www.scielo.sa.cr/scielo.php?script=sci_arttext&pid=S1409-00152013000100009