%0 Journal Article
%T NEURODEGENERATION WITH IRON ACCUMULATION TYPE1
%A Shrikhande D Y
%A Ahya K
%A Shedabale D
%A Garg G
%J Pravara Medical Review
%D 2010
%I Pravara Institute of Medical Sciences (DU), Loni
%X Neurodegeneration with iron accumulation type 1 is a rare degenerative disorder presenting with dementia and progressive extrapyramidal dysfunction. A 10 yrs old girl reported with complaints of difficulty in speech and involuntary movements. MRI Brain showed ¡®eye of tiger appearance¡¯ which is suggestive of neurodegeneration with iron accumulation type 1. Treatment is symptomatic and chelating agents have no effect. The disease is progressivelyfatal
%K Neurodegeneration with iron accumulation type 1
%K Hallervorden-Spatz
%U http://www.pravara.com/pmr/pmr-5-1-8.pdf