%0 Journal Article %T S¨ªndrome de Marcus Gunn. Presentaci¨®n de un caso Marcus Gunn syndrome. A case report %A Sahely Sixto Fuentes %A Annia Dolores Gorte Qui£¿ones %A Kenia Ramos Padilla %A Humberto Vald¨¦s Hern¨¢ndez %J Revista de Ciencias M£¿£¿dicas de Pinar del R£¿-o %D 2011 %I Editorial Ciencias M¨¦dicas %X El fen¨®meno de Marcus Gunn es un movimiento cong¨¦nito asociado trig¨¦mino oculomotor que afecta a los m¨²sculos elevadores del p¨¢rpado y los de la masticaci¨®n. Se presenta la ptosis asociada a una sincinesia, que consiste en la elevaci¨®n involuntaria del p¨¢rpado pt¨®sico, relacionado con movimientos de desplazamiento lateral de la mand¨ªbula o de abertura de la boca. Suele ser m¨¢s frecuente en ni as y en el ojo izquierdo, y ocasionalmente, se presenta una par¨¢lisis de recto superior del mismo lado. De forma extremadamente rara se asocia con anomal¨ªas sist¨¦micas. Algunos autores refieren que este fen¨®meno se hace menos evidente con la edad. Se presentan las caracter¨ªsticas oftalmol¨®gicas y cl¨ªnicas de un paciente a quien se le diagnostic¨® este s¨ªndrome asociado a anomal¨ªas sist¨¦micas. El diagn¨®stico precoz de esta patolog¨ªa nos posibilita la prevenci¨®n de la ambliop¨ªa y sus secuelas. Marcus Gunn phenomenon is a congenital movement associated with the trigeminus-oculomotor nerve which affects the levator palpebrae superioris and the mastication muscles. Ptosis associated with synkinesis is presented and it consists of the involuntary synchronic (ptosis) eyelid elevation, related to the movements of lateral displacement of the jaw or when opening the mouth, which is frequently found in girls in left eye; occasionally rectus superioris paralysis of left side is also observed. It is rarely associated with systemic anomalies. Some authors consider that this phenomenon is less evident as the years pass. The ophthalmologic and clinical features of a patient that was diagnosed with this syndrome in association with systemic anomalies is presented. The early diagnosis of this pathology makes the prevention of amblyopia and its sequela possible. %K ENFERMEDADES OCULARES %K ANOMAL¨ªAS DEL OJO %K EYE DISEASES %K EYE ABNORMALITIES %U http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S1561-31942011000300020