%0 Journal Article
%T RABSON-MENDENHALL SYNDROME: A CASE REPORT
%A Mohammad Reza ALAEI
%A Seyed Alireza MIRJAVADI
%A Reza SHIARI
%J Iranian Journal of Child Neurology
%D 2010
%I Iranian Child Neurology Society
%X Rabson-Mendenhall syndrome is a rare genetic disorder characterized by growth retardation, dysmorphisms, lack of subcutaneous fat, acanthosis nigricans, enlarged genitalia, hirsutism, dysplastic dentition, coarse facial features, paradoxical fasting hypoglycemia, postprandial hyperglycemia, extreme hyperinsulinemia and pineal hyperplasia. Herein, we described a 10- year-old girl with physical features of the Rabson-Mendenhall syndrome that was presented with polyuria. To our knowledge, this is the first report of the Rabson-Mendenhall syndrome from Iran.
%K Diabetes
%K Hirsutism
%K Insulin resistance
%K Clitoromegaly
%U http://journals.sbmu.ac.ir/ijcn/article/view/1726/1527