%0 Journal Article
%T Enfermedad de moyamoya, macrocefalia y d谷ficit intelectual en un adolescente Moyamoya disease, macrocephaly and intellectual impairment in an adolescent
%A Jos谷 Vargas D赤az
%A Nicol芍s Gar車falo G車mez
%A Esperanza Barroso Garc赤a
%A Adnolys Reyes Beraza赤n
%J Revista Cubana de Pediatrˋ-a
%D 2013
%I Editorial Ciencias M谷dicas
%X El patr車n moyamoya se caracteriza por un estrechamiento cr車nico progresivo de la porci車n terminal de la arteria car車tida interna o sus principales ramas terminales principalmente. Los ni os con moyamoya t赤picamente se presentan con ictus arteriales isqu谷micos, o con accidentes isqu谷micos transitorios. Se presenta el caso cl赤nico de un adolescente, con d谷ficit intelectual y macrocr芍nea, con evidencia en los estudios de resonancia magn谷tica nuclear cerebral de infartos arteriales isqu谷micos a repetici車n, e im芍genes sugestivas de moyamoya, y se comprueba el patr車n moyamoya por angiograf赤a de sustracci車n digital. Comprobado el diagn車stico de enfermedad de moyamoya, el objetivo con este enfermo fue tratar de mejorar la irrigaci車n cerebral, planteando la necesidad de someter al paciente a cirug赤a de revascularizaci車n, y, mientras esto no fuera posible, usar aspirina como antiagregante plaquetario, en un intento de impedir o disminuir el riesgo de nuevos infartos cerebrales o de accidentes transitorios isqu谷micos a repetici車n. The moyamoya pattern is characterized by chronic progressive narrowing of the terminal portion of the internal carotid artery or of its main terminal branches. Children suffering moyamoya disease regularly present with ischemic arterial ictus or transient ischemic strokes. Here is the case of an adolescent with intellectual impairment and macrocrania. The magnetic resonance imaging study of his brain showed repeated ischemic arterial infarctions and images suggestive of moyamoya disease, the pattern of which was later confirmed by digital subtraction angiography. The first objective was to intend to improve his cerebral irrigation by performing a revascularization surgery, but as long as this action was not accomplished, then taking aspirin as anti-platelet aggregation drug could prevent or reduce the risk of new cerebral infarctions or of repeated transient ischemic strokes.
%K s赤ndrome de moyamoya
%K enfermedad de moyamoya
%K ictus isqu谷micos en pediatr赤a
%K enfermedad cerebrovascular en ni os
%K moyamoya syndrome
%K moyamoya disease
%K ischemic ictus in pediatrics
%K cerebrovascular disease in children
%U http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S0034-75312013000100011