%0 Journal Article
%T S赤ndrome dienc谷falico como causa de desnutrici車n severa Diencephalic syndrome as a cause of severe malnutrition
%A Leonor B芍ez Segurola
%A Rafael Jim谷nez Garc赤a
%A Eduardo Piˋeiro Fern芍ndez
%A Evelio P谷rez Mart赤nez
%J Revista Cubana de Pediatrˋ-a
%D 2013
%I Editorial Ciencias M谷dicas
%X El s赤ndrome diencef芍lico es un complejo de s赤ntomas y signos causados por disfunci車n de esta 芍rea del enc谷falo caracterizado por una marcada desnutrici車n aun cuando la ingesta cal車rica es normal. Se presentan dos casos, el primero de ellos una ni a de 13 meses de edad con antecedentes de un fallo de medro a partir del tercer mes de vida, que ingres車 en este servicio para el estudio de una desnutrici車n proteico energ谷tica severa que present車 en el transcurso de su evoluci車n un apetito inestable y al mes de ingresada un evento parox赤stico. Se le realiz車 resonancia magn谷tica nuclear y se comprob車 imagen hipodensa, redondeada, que med赤a aproximadamente 3 x 3 cm en regi車n supraselar; fue intervenida quir迆rgicamente en 2 ocasiones, se realiz車 ex谷resis del tumor, y se confirm車 anatomopatol車gicamente un astrocitoma piloc赤tico de bajo grado. El segundo paciente, un lactante que ingres車 con el diagn車stico confirmado de tumor intracraneal para estudio, semejante al caso presentado anteriormente, mostraba una marcada desnutrici車n proteico energ谷tica, se le realiz車 tomograf赤a axial computarizada en la que se pudo apreciar una extensa masa tumoral supraselar con dilataci車n del sistema ventricular. Durante su evoluci車n present車 marcada anorexia con p谷rdida de peso progresiva, por lo que se realiz車 gastrostom赤a. A los 59 d赤as falleci車 como consecuencia de una pancitopenia, y la necropsia concluy車: astrocitoma piloc赤tico de bajo grado. Diencephalic syndrome is a set of symptoms and signs caused by dysfunction in this area of the encephalon and characterized by marked malnutrition despite adequate intake of calories. Two cases were reported in this paper. The first one was a 13-years old girl with a history of medro failure since her 3rd month of life, who was admitted to this service for the study of her severe protein/energy malnutrition. In the course of her hospitalization, she presented with unstable appetite and suffered a paroxistic event one month after being hospitalized. The infant girl was then performed magnetic resonance imaging test which revealed a 3 cm x 3cm rounded hypodense image in the suprasellar region. She was operated on twice, the tumor was excised and the anatomic and pathological analysis yielded the presence of low grade pilocytic astrocytoma. The second patient was an small infant who was admitted to the service with a confirmed diagnosis of intracranial tumor for study, very similar to the case previously presented. He suffered an acute protein/energy malnutrition, so he was performed a computerized tomography which showed a broad tumoral mas
%K s赤ndrome diencef芍lico
%K desnutrici車n
%K caquexia-anorexia
%K diencephalic syndrome
%K malnutrition
%K cachexia-anorexia
%U http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S0034-75312013000100012