%0 Journal Article %T S¨ªndrome de Axenfeld-Rieger con glaucoma asociado Axenfeld-Rieger syndrome associated with glaucoma %A Yanileidy Blanco Gonz¨¢lez %A Teresita de Jes¨²s M¨¦ndez S¨¢nchez %A Liamet Fern¨¢ndez Argones %A Daniel L¨®pez Felipe %J Revista Cubana de Oftalmolog£¿-a %D 2012 %I Editorial Ciencias M¨¦dicas %X Se describen dos casos cl¨ªnicos con s¨ªndrome de Axenfeld-Rieger y glaucoma bilateral. El primer caso representa una paciente femenina con corectopia, embriotoxon posterior, atrofia del estroma anterior del iris, adherencias iridocorneales y glaucoma bilateral; por lo que se decide realizar trab¨¦culo-trabeculectom¨ªa en ambos ojos y mantuvo cifras de tensi¨®n intraocular dentro de l¨ªmites normales al a o de evoluci¨®n. El segundo caso se trata de un paciente masculino con escleras azules, microc¨®rnea, embriotoxon posterior, aniridia parcial, atrofia sectorial del iris y glaucoma bilateral; por lo que se realiz¨® trab¨¦culo-trabeculectom¨ªa de ambos ojos con descompensaci¨®n posterior del ojo izquierdo. Se inici¨® el tratamiento m¨¦dico sin buenos resultados y se reintervino el ojo izquierdo, se descompens¨® dos meses despu¨¦s de la cirug¨ªa. Actualmente se encuentra compensado con tratamiento m¨¦dico. Two clinical cases of Syndrome of Axenfeld-Riegel and bilateral glaucoma were described. The first case was a female patient with corectopia, posterior embriotoxon, atrophy of the anterior stroma of the iris, iridocorneal adherences and bilateral glaucoma. To treat her, it was decided to perform trabeculo-traceculectomy in both eyes and as a result, the patient kept intraocular pressure values within the normal limits after one year. The second case was male patient who suffered with blue sclera, microcornea, posterior embrotoxon, partial aniridia, sector atrophies of the iris and bilateral glaucoma. Trabeculo-trabeculectomy of both eyes with posterior decompensation of the left eye was applied. The medical treatment did not yield good results, His left eye was then re-operated and two month afterwards, decompensation occurred again. At present, he is compensated with a new medical treatment. %K s¨ªndrome de Axenfeld-Rieger %K glaucoma cong¨¦nito %K ni o %K Axenfeld-Rieger¡¯s syndrome %K congenital glaucoma %K child %U http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S0864-21762012000300014