%0 Journal Article
%T F赤stula biliobronquial, una rara complicaci車n de PKD-1: a rare complication of PKD-1 Bronchiobiliary fistula
%A L芍zaro L. Capote Pereira
%A Sigifredo Montero Ferrer
%A Ana E. Mera Fern芍ndez
%A Eliseo Capote Leyva
%J Revista Cubana de Medicina Militar
%D 2006
%I ECIMED
%X La enfermedad renal poliqu赤stica autos車mica dominante (PKD-1) es la nefropat赤a hereditaria m芍s frecuente y constituye una causa importante de insuficiencia renal cr車nica terminal. La f赤stula biliobronquial resulta una rara complicaci車n secundaria a infecciones como Equinococcus granuloso y amebiasis, traumas y enfermedad maligna. Se manifiesta frecuentemente con expectoraci車n de bilis (biliptisis) y s赤ntomas respiratorios. Se presenta una paciente de 65 a os de edad, de la raza blanca, con PKD-1 e insuficiencia renal cr車nica, con s赤ntomas respiratorios y biliptisis secundaria a una f赤stula biliobronquial. Se confirm車 el diagn車stico con la demostraci車n del trayecto fistuloso en el par谷nquima hep芍tico y la presencia de bilis en el par谷nquima pulmonar por la tinci車n de Fouchet. Se concluye que PKD-1 es una rara causa de f赤stula biliobronquial y un diagn車stico que se debe sumar a las ya conocidas causas de esta complicaci車n. Autosomal dominant polycystic kidney disease (PKD-1) is the most frequent inherited nephropathy and constitutes an important cause of terminal chronic kidney failure. Bronchiobiliary fistula is a rare complication secondary to infections like granular Equinococcus and amebiasis, trauma and malignant disease. Frequent manifestations of this disease are bile expectoration (biliphthisis) and respiratory symptoms. The case of a 65 years-old Caucasian female patient suffering from PKD-1 and chronic kydney failure, with respiratory symptoms and biliphthisis secondary to a bronchiobiliary fistula was presented. The diagnosis was confirmed with the demonstration of the fistulous path in the hepatic parenchyma and the presence of bile in the pulmonary parenchyma by means of Fouchet∩s stain. It was concluded that PKD-1 is a rare cause of bronchiobiliary fistula and a diagnosis that must be added to the already known causes of this complication.
%K Enfermedad poliqu赤stica renal autos車mica dominante (PKD-1)
%K f赤stula biliobronquial
%K biliptisis
%K insuficiencia renal cr車nica
%K Autosomal dominant polycystic kidney disease (PKD-1)
%K bronchiobiliary fistula
%K biliphthisis
%K chronic kidney failure
%U http://scielo.sld.cu/scielo.php?script=sci_arttext&pid=S0138-65572006000200009