%0 Journal Article %T S¨ªndrome de Sj gren primario con neumon¨ªa intersticial linfoc¨ªtica y enfermedad qu¨ªstica pulmonar Primary Sj gren's syndrome with lymphocitic interstitial pneumonia and cystic pulmonary disease %A Jimi Mej¨ªa-Vallejo %A Jorge Carrillo-Bayona %A Antonio Iglesias-Gamarra %A Federico Rond¨®n %J Revista Colombiana de Reumatolog¨ªa %D 2007 %I Asociaci¨®n Colombiana de Reumatolog¨ªa %X El s¨ªndrome de Sj gren primario (SSP) es una exocrinopat¨ªa autoinmune cr¨®nica caracterizada por infiltraci¨®n linfoc¨ªtica de tejido glandular y extraglandular; el compromiso pulmonar es heterog¨¦neo; el objetivo del presente estudio es informar el primer caso en Colombia de SSP con neumon¨ªa intersticial linfoc¨ªtica y enfermedad qu¨ªstica pulmonar, plantear diagn¨®sticos diferenciales, abordaje diagn¨®stico y alternativas terap¨¦uticas. The primary Sj gren's syndrome (PSS) is a chronic autoimmune exocrinopathy characterized by lymphocytic infiltration of glandular and extraglandular tissue, the lung involvement is heterogeneous; the aim of this study is report the first case in Colombia of PSS with lymphocytic intersticial pneumonia and cystic pulmonary disease discuss differential diagnosis and the initial diagnostic and therapeutic work up. %K s¨ªndrome de Sj gren primario %K enfermedad pulmonar qu¨ªstica %K neumon¨ªa intersticial linfoc¨ªtica %K primary Sj gren's syndrome %K cystic lung disease %K lymphocytic interstitial pneumonia %U http://www.scielo.org.co/scielo.php?script=sci_arttext&pid=S0121-81232007000300006