%0 Journal Article %T S¨ªndrome pulm¨®n ri ¨®n en vasculitis sist¨¦mica por inmunoglobulina A secundaria a linfoma Lung-kidney sindrome in systemic vasculitis by inmunoglobulin A due to lymphoma %A David Andr¨¦s Ocampo Ram¨ªrez %A C¨¦sar A Restrepo Valencia %J Revista Colombiana de Reumatolog¨ªa %D 2012 %I Asociaci¨®n Colombiana de Reumatolog¨ªa %X Paciente de 35 a os de edad, quien debuta con s¨ªndrome de pulm¨®n ri ¨®n secundario a vasculitis pulmonar y dep¨®sitos renales granulosos de IgA, en quien se diagnostica vasculitis sist¨¦mica por IgA, posteriormente, presenta compromiso pancre¨¢tico y cut¨¢neo (P¨²rpura de Henoch - Sch nlein), falleciendo ocho meses m¨¢s tarde por linfoma difuso de c¨¦lulas B de alto grado. Este es el reporte de caso n¨²mero catorce en el que se establece asociaci¨®n entre neoplasia hematol¨®gica y P¨²rpura de Henoch - Sch nlein. Patient was 35-years-old who presents with kidney-lung syndrome secondary to pulmonary vasculitis and renal granular deposits of IgA, in whom systemic vasculitis IgA was diagnosed, and then he had cutaneous and pancreatic involvement (Henoch Sch nlein Purpura). He died eight months later by diffuse high grade B-cell lymphoma. This is the number fourteen case report of an association between hematological malignancy and Henoch - Sch nlein. %K P¨²rpura de Henoch - Sch nlein %K s¨ªndrome pulm¨®n ri ¨®n %K linfoma difuso de c¨¦lulas B de alto grado %K Henoch - Sch nlein Purpura %K kidney-lung syndrome %K diffuse high grade B-cell lymphoma %U http://www.scielo.org.co/scielo.php?script=sci_arttext&pid=S0121-81232012000200007