%0 Journal Article %T Peliosis hepatoespl谷nica. Informe de un caso y revisi車n de la literatura: A case report and a literature review Hepatosplenic peliosis %A Pila P谷rez %A Rafael Pila Pel芍ez %A Pedro Rosales Torres %A V赤ctor Holgu赤n Prieto %J Revista Colombiana de Gastroenterologia %D 2012 %I Asociaci車n Colombiana de Gastroenterolog赤a %X La peliosis es una entidad benigna muy rara, que se caracteriza por cavidades repletas de sangre dentro de 車rganos s車lidos, principalmente en el sistema reticuloendotelial. La peliosis puede tambi谷n afectar otros 車rganos como pulmones, pleura, ri ones, gl芍ndulas suprarrenales y est車mago. Las lesiones pueden ser 迆nicas o m迆ltiples y de tama o variable. La etiolog赤a es ignorada, pero se ha relacionado con la ingesti車n o contacto con f芍rmacos y t車xicos diversos como esteroides y anticonceptivos orales, asoci芍ndose a enfermedades tumorales hematol車gicas y a enfermedades infecciosas, en particular a la tuberculosis; en algunos casos es idiop芍tica. Presentamos el caso de una mujer de 60 a os con antecedentes de hipertensi車n arterial. La exploraci車n f赤sica y los estudios de imagen evidenciaron una hepatomegalia nodular gigante sin esplenomegalia. Los ex芍menes de laboratorio indicaron trastornos propios de insuficiencia hep芍tica y la paciente fallece por shock hipovol谷mico y hemoperitoneo. El estudio necr車psico determin車 la existencia de una peliosis hepatoespl谷nica parenquimatosa "mayor" de etiolog赤a idiop芍tica. Se lleva a cabo una revisi車n de la literatura, se alando aspectos relacionados con historia, patog谷nesis, etiolog赤a, aspectos cl赤nicos, diagn車sticos y terap谷uticos. Peliosis is a very rare benign entity which is characterized by blood filled cavities filled within solid organs. They occur primarily in the mononuclear phagocyte system although peliosis can also affect organs such as the lungs, pleura, kidneys, adrenal glands and stomach. Only one lesion or multiple lesions may occur, and their size is also variable. The etiology is unknown but is related to ingestion of, or direct contact with, drugs and various toxic substances such as steroids and oral contraceptives. It is associated with hematologic cancers and infectious diseases, particularly tuberculosis. In some cases it is idiopathic. We present the case of a 60 years old woman with a history of hypertension. Physical examination and various imaging studies showed a giant nodular hepatomegaly without splenomegaly. Laboratory studies showed disorders due to liver failure. The patient finally died of hypovolemic shock and hemoperitoneum. An autopsy determined the presence of parenchymal hepatosplenic peliosis of other than idiopathic etiology. A literature review highlighting the history, pathogenesis, etiology, clinical aspects, diagnosis and treatment of hepatosplenic peliosis is included. %K Peliosis %K hepatomegalia %K hemoperitoneo %K Peliosis %K hepatomegaly %K hemoperitoneum %U http://www.scielo.org.co/scielo.php?script=sci_arttext&pid=S0120-99572012000100006