%0 Journal Article %T Malformaci車n linfangiomatosa intestinal con tejido pancre芍tico ect車pico: A prop車sito de un caso y revisi車n de la literatura Intestinal lymphangiomatosis with ectopic pancreatic tissue: A case report and literature review %A Selena Torga S %A Luc赤a Raposo R %A Esther Yag邦e Z %A Nataliz Vega M %J Revista Chilena de Radiolog赤a %D 2012 %I Publimpacto %X La malformaci車n linfangiomatosa intestinal es una entidad poco frecuente, t赤pica de la edad pedi芍trica, cuya etiopatogenia es desconocida, aunque se barajan varias hip車tesis. Presentamos un caso de linfangiomatosis intestinal con tejido pancre芍tico ect車pico mesent谷rico, una asociaci車n no descrita anteriormente en la literatura. Destacamos la importancia de conocer que esta entidad, en ocasiones, se asocia a otro tipo de malformaciones intrabdominales, incluso no descritas previamente en la literatura. Se debe plantear como el primer diagn車stico diferencial durante la edad pedi芍trica, ante el hallazgo radiol車gico de lesiones qu赤sticas mesent谷ricas, confirmando posteriormente mediante un estudio anatomopatol車gico de las lesiones. Intestinal lymphangiomatosis is a rare malformation typically affecting children. Its etiology is unknown, although several hypotheses have been proposed. We present a case of intestinal lymphangiomatosis with ectopic pancreatic tissue of the mesentery, an association not previously described in literature. We emphasize the fact that this entity has sometimes been associated with other intra-abdominal malformations, even conditions undescribed in scientific literature. It must be considered the first differential diagnosis for pediatric patients with radiological evidence of mesenteric cystic lesions, subsequently confirmed by pathological examination. %K Dolor abdominal %K Linfangiomatosis %K Linfangiectasia intestinal %K Mesenterio %K Abdominal pain %K Intestinal Lymphangiectasis %K Lymphangiomatosis %K Mesentery %U http://www.scielo.cl/scielo.php?script=sci_arttext&pid=S0717-93082012000200006