%0 Journal Article
%T Systemic sclerosis in a patient with pityriasis rubra pilaris
%A Faten Frikha
%A Makram Frigui
%A Hatem Masmoudi
%A Hamida Turki
%J Pan African Medical Journal
%D 2010
%I African Field Epidemiology Network
%X Pityriasis rubra pilaris (PRP) is a rare, chronic erythematous squamous disorder of unknown etiology. It has been found in association with several autoimmune diseases, including thyroiditis, myositis, myasthenia gravis and vitiligo. Herein we report a case of systemic sclerosis in a patient with classic adult pityriasis rubra pilaris. A 38 year old woman with classic adult type 1 pityriasis rubra pilaris (PRP) developed progressive skin thickening of the trunk, face, upper and lower extremities after 2 years of PRP treatment with topical emollients and steroids. Clinical examination and immunological findings were consistent with SSc. Co-existence of these two rare conditions is documented for the first time
%K Systemic sclerosis
%K pityriasis rubra pilaris
%K skin disease
%K autoimmune disease
%K acroosteolysis
%K rare diseases
%U http://www.panafrican-med-journal.com/content/article/6/6/pdf/6.pdf