%0 Journal Article
%T Genital Hailey- Hailey disease: a case report
%A Deeptara Pathak Thapa
%A Anil Kumar Jha
%A Sujata Pudasaini
%A Chandani Kharel
%J Our Dermatology Online
%D 2013
%I Our Dermatology Online
%X Hailey ¨C Hailey disease is a rare autosomal dominant acantholytic disorder, previously not reported from Nepal. We report a case of 30 years old female who presented with pruritic hyperkeratotic papules and plaques on vulva, perianal area and inner left thigh for a period of one year. Biopsy from the lesion showed suprabasal acantholysis with loss of intercellular bridges resulting in a dilapidated brick-wall appearance; characteristic of Hailey ¨C Hailey disease. Treatment of this disease till date is far from satisfactory.
%K acantholysis
%K Hailey ¨C Hailey disease
%K Nepal
%U http://www.odermatol.com/issue-in-html/2013-1-18-genital/