%0 Journal Article
%T Abnormal Dentition in a Boy with Incontinentia Pigmenti: Case Report
%A H Afshar
%A M Daneshpazhooh
%A A Kiani
%A P Aref
%J Journal of Dentistry of Tehran University of Medical Sciences
%D 2012
%I Tehran University of Medical Sciences
%X Incontinentia pigmenti (IP) is an X-linked dominant genodermatosis characterized by typical skin lesions along Blaschko¡¯s lines and associated with ocular, dental, nails, hair, skeletal, central nervous system and cardiovascular anomalies. We report a 5-year-old boy with cutaneous hyperpigmentation along Blaschko¡¯s lines, atrophic streaks, strabismus and mental retardation. He showed the characteristic abnormal dentition seen in IP as partial hypodontia, peg-shaped anterior teeth and un-erupted teeth. The expression of IP in boys is exceptional as the disease is lethal in males.
%K Incontinentia Pigment
%K Dentition
%K Male
%U http://jdt.tums.ac.ir/index.php/jdt/article/view/793/365