%0 Journal Article
%T Un caso raro de malformaci¨®n del tubo neural: s¨ªndrome de hendidura notocordal
%A Gonz¨¢lez de Chirivella
%A Xiomara
%A Betancourt
%A Zuray
%A Gonz¨¢lez
%A Mari¨¢ngela
%J Revista de Obstetricia y Ginecolog¨ªa de Venezuela
%D 2009
%I Sociedad de Obstetricia y Ginecolog¨ªa de Venezuela
%X a 33 years old woman, gravida ii, para i, was referred at 27 weeks gestation with the diagnosis of fetal ascites. ultrasound report showed, polyhydramnios, fetal abdomen distended occupied by a large liquid mass initially impressed as fetal ascites, echogenic bowel is also consistent with meconium peritonitis and polymicrogiria. in a subsequent ultrasonography was observed column defect on the sacrum where emerges a cystic mass equivalent to the known "anterior spina bifida", others previous ultrasound findings were confirmed. cesarean section was performed at 33 weeks gestation, obtaining male live newborn, 2 820 g and 45 cm in length, with apgar score of 6 y 7 at 1 and 5 minutes, respectively. the newborn presented transient distress respiratory syndrome and symptoms of intestinal obstruction which was resolved surgically. operative findings: intestinal atresia, and confirming the split notochord syndrome. the newborn died of sepsis. no autopsy was performed. commentary: the ultrasound findings depend on the form of the lesion, but often are abdomino-thoracic cysts, myelomeningocele and spina bifida. the prognosis is usually ominous, but depends on the extent of the lesions and associated anomalies.
%K split notochord syndrome
%K meconial peritonitis
%K intestinal atresia
%K fetal ascites
%K polyhydramnios.
%U http://www.scielo.org.ve/scielo.php?script=sci_abstract&pid=S0048-77322009000400009&lng=en&nrm=iso&tlng=en