%0 Journal Article
%T The Destombes-Rosai-Dorfman Disease or Sinus Histiocytosis with Massive Lymphadenopathy: A Rare Case Described in the Paediatrics Department of Yalgado Ouedraogo University Hospital
%A Chantal Zoungrana-Ouattara
%A Flore Ou¨¦draogo
%A Laure Toguy¨¦ni
%A Ang¨¨le Kalmogho
%A Caroline Yonaba
%A Chantal Gabrielle Bouda
%A Rolande Kabor¨¦
%A Fla Kou¨¦ta
%J Open Journal of Pediatrics
%P 345-352
%@ 2160-8776
%D 2017
%I Scientific Research Publishing
%R 10.4236/ojped.2017.74039
%X Destombes-Rosai-Dorfman¡¯
disease (DRD) is an inflammatory non-langerhansian</span><span style=\"font-family:&quot;\"><span style=\"font-family:Verdana;\"> histiocytosis with adenomegaly. It is a rare histiocytic disorder worldwide,
less than 1000 reported cases. It is of unknown etiology and is characterized
in its classical form by multiple adenomegalia, especially localized at
cervical area, </span><span style=\"font-family:Verdana;\">but also at mediastinal,
axillary and inguinal area</span></span><span style=\"font-family:Verdana;\">s</span><span style=\"font-family:Verdana;\">. It is a benign condition,
even</span><span style=\"font-family:&quot;\"><span style=\"font-family:Verdana;\"> if </span><span style=\"font-family:Verdana;\">it is
deforming, with spontaneously resolving evolution. We report a case of</span><span style=\"font-family:Verdana;\"> DRD </span><span style=\"font-family:Verdana;\">disease in a 13-year-old girl,
hospitalized in the Department of Pediatrics of</span> <span style=\"font-family:Verdana;\">the </span><span style=\"font-family:Verdana;\">Yalgado Ou¨¦draogo
University Hospital Center in Ouagadougou, in March</span><span style=\"font-family:Verdana;\"> 2015. She was
admitted for a voluminous bilateral painless cervical swelling, with no sign of
local compression, having been operating for about a year. Biological tests
showed signs of chronic inflammation; the imagery specified the benign
character of these formations: adenomegalia. Confirmation of the diagnosis was
made by pathological examination, describing the aspect of emperipolesis to
histology and, immunohistochemistry, polytypic plasmacytosis and PS100
positive/CD1a histiocytosis negative. The treatment could not be </span><span style=\"font-family:Verdana;\">properly carried out, in view of the early
discharge, against medical advice</span><span style=\"font-family:Verdana;\"> from the patient. The evolution would
have been marked, according to the parents, by a slight involution of swelling.
%K Destombes-Rosai-Dorfman Disease
%K Emperipolesis
%K Immunohistochemistry
%K Yalgado Ouedraogo University Hospital
%U http://www.scirp.org/journal/PaperInformation.aspx?PaperID=81237