%0 Journal Article %T Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia %A Peter G. Pavlidakey %A Alok Mohanty %A Lisa J. Kohler %A Howard J. Meyerson %J Case Reports in Hematology %D 2011 %I Hindawi Publishing Corporation %R 10.1155/2011/941637 %X Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma. %U http://www.hindawi.com/crim/hematology/2011/941637/