%0 Journal Article %T Xantogranulomatosis orbitaria: Enfermedad de Erdheim-Chester Orbit Xanthogranulomatosis: Erdheim-Chester disease %A P Rozas Reyes %A A Seˋaris Gonz芍lez %A CM Gonz芍lez Rodr赤guez %J Archivos de la Sociedad Espaˋola de Oftalmolog赤a %D 2004 %I Scientific Electronic Library Online %X Caso cl赤nico: Paciente con edema bilateral de p芍rpados superiores y lesiones similares a xantelasmas de tres a os de evoluci車n. La exploraci車n oftalmol車gica mostraba dos tumoraciones temporales sim谷tricas en ambos p芍rpados superiores con lesiones naranjo-amarillentas. Se pautaron corticoides que hicieron disminuir el tama o de las tumoraciones, con recidiva de los mismos al suspender dicha medicaci車n. La biopsia revel車 una xantogranulomatosis palpebral. El resto de las exploraciones sist谷micas fueron normales. Discusi車n: La enfermedad de Erdheim-Chester es una xantogranulomatosis que puede afectar a las estructuras oculares y periorbitarias. La combinaci車n de lesiones similares a xantelasmas y masas orbitarias bilaterales deben hacernos pensar en este proceso y buscar la posible afectaci車n sist谷mica. Case report: A patient was studied because of upper lid bilateral edema and xanthelasmae-like lesions after three years of evolution. During the ophthalmologic examination orange-yellowish lesions and two symmetrical tumours were observed on the temporal part of both upper lids. Corticoid-therapy was undertaken which reduced the size of the tumours, however the size increased again after the discontinuation of treatment. A biopsy was performed and lid xanthogranulomatosis was diagnosed. Other systemic examinations were normal. Discussion: Erdheim-Chester disease is a xanthogranulomatosis that can affect ocular and periorbital structures. Combination of xanthelasmae-like lesions and bilateral orbital masses should make us consider this process and try to locate any associated systemic conditions. %K Xantoganulomatosis %K Erdheim-Chester %K Xanthogranulomatosis %K Erdheim-Chester disease %U http://scielo.isciii.es/scielo.php?script=sci_arttext&pid=S0365-66912004001000009