article, we present the case of a 12-year-old girl with sickle cell disease (SCD), who presented with the severe headache.
She had bilateral 6th cranial nerve palsy and papilloedema. The common sickle
cell-related vascular causes of headache were ruled
out by neuro-imaging. She then had a lumbar puncture and was diagnosed with
idiopathic intracranial hypertension
(IIH). This case demonstrates that IIH can affect younger children with SCD and
should form a part of differential diagnosis when investigating causes of
headache in SCD.