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Klippel-Trenaunay Syndrome and Pregnancy  [PDF]
Tu?ba Güngor Gündo?an,Y. Jacquemyn
Obstetrics and Gynecology International , 2010, DOI: 10.1155/2010/706850
Abstract: Klippel-Trenaunay syndrome is a rare congenital vascular disorder, and only few cases have been described in pregnancy. We describe two cases, in one patient without complications, the other patient developed postpartum deep venous thrombosis. 1. Introduction Klippel-Trenaunay syndrome is a congenital vascular disorder characterized by cutaneous hemangiomas, venous varicosities, and limb hypertrophy. Both obstetric and anesthetic management in these cases can be rather complicated. We report on two cases. Case 1. A 33-year Caucasean woman had the diagnosis of Klippel-Trenaunay syndrome at age 5. As a child, some of the hemangiomata on the lower limb had been irradiated with radioactive cobalt. No further details on her childhood therapy could be found. Her body weight was 63?kg. She had never suffered any thrombosis. During pregnancy, low-molecular-weight heparine nadroparin was started from 12 weeks on (nadroparin single daily subcutaneous dose 0.3?mL) (i.e., 2850 anti Xa, injection of Fraxiparine, Glaxo Smith Kline, Genval, Belgium), because the patient complained of progressive painful swelling and pain in the right leg; Doppler examination demonstrated no thrombosis. At 36 weeks of gestational age, magnetic resonance image (MRI) of the lumbosacral region was performed which demonstrated some dilation of the anterior epidural venous plexus at the level lumbal 4-lumbal 5, but no arguments for an arteriovenous or venous malformation in the spinal canal. At 39 weeks, she went into spontaneous labour and had a spontaneous delivery of a baby girl, weighting 2770 gram, Apgar 8 and 9 after 1 and 5 minutes. She received 10?IU of oxytocine as prevention for postpartum hemorrhage, this is a standard procedure for all patients in our center. The subcutaneous low-molecular-weight heparine was continued for six weeks after delivery. There were no problems in the postpartum period. Case 2. A 36-year-old Caucasean woman presented for a first pregnancy. Diagnosis of Klippel-Trenaunay syndrome was made shortly after birth. She suffered from hypertrophy of the right leg 4?cm longer than left leg, atypically localized varices with an absent deep venous system at the right leg, and port-wine stains in multiple dermatomes on the right leg, abdomen, thorax, neck, face, and arms for which she had received cutaneous lasertherapy. There was no history of thrombosis. During pregnancy, no low-weight heparine nor low-dose acetylsalicylic acid was given. The patient did not demonstrate any change in her lower limbs during pregnancy. At 36 weeks, MRI of the lumbosacral spine
Klippel-Trenaunay Syndrome - A Case Report  [PDF]
Anju kapoor, Dipankar Sarkar, *Garjesh Singh Rai, **Shweta Anand
People's Journal of Scientific Research , 2012,
Abstract: Klippel-Trenaunay Syndrome (KTS) is a sporadic disorder characterized by the triad of vascular malformation (capillary hemangioma or port wine stain), venous varicosity and soft tissue and/ or bony hypertrophy. We report here a case of Klippel-Trenaunay syndrome with review of literature.
Klippel Trenaunay Syndrome  [cached]
Miranda M.F,Chahal N.H
Indian Journal of Dermatology , 2001,
Abstract: A classical case of klippel trenaunay syndrome in a 25 year old male characterized by port wine stain, varicose and increase in length of the right lower extremity associated with ulceration is presented.
Klippel trenaunay syndrome associated with unusual eye changes  [cached]
Mohan L,Mukhija R,Arora S,Prasad V
Indian Journal of Dermatology, Venereology and Leprology , 1990,
Abstract: A young female had Klippel-Trenaunay syndrome with involvement from the head the toe on the left ide. The radiological, ophthalmological and histopathological findings were consistent with Klippel-Trenaunay syndrome. The unique feature was negalocornea which has not been reported earlier.
Pregnancy and Klippel-Trenaunay Syndrome—A Case Report  [PDF]
María Jesús Cancelo Hidalgo, Gisselle Adriana González Segura, Laura Yago Lisbona, Estherde la Viuda García
Case Reports in Clinical Medicine (CRCM) , 2014, DOI: 10.4236/crcm.2014.37095
Abstract:

Klippel-Trenaunay Syndrome (KTS) is a rare triad of congenital vascular malformations involving extensive Port wine stains, soft tissue or bone hypertrophy and underlying venous and/or lymphatic malformation affecting limb, pelvicor abdominal organs. Pregnancy is known to exacerbate KTS complications and can put women at increased obstetrical risk due to deep venous thrombosis and other thromboembolic events. We report a case of a pregnant woman with KTS with the personal antecedent of two episodes of pulmonary thromboembolism.

Klippel-Trenaunay Syndrome With Naevus Unius Lateris  [cached]
Chanda M,Gangopadhyay D N,Senapati S,Dutta R N
Indian Journal of Dermatology , 2000,
Abstract: A case of Klippel-Trenaunay syndrome with naevus unius lateris is reported here for this rare association. Search of Indian literature failed to show any such report in the past.
Klippel-Trenaunay syndrome with gastrointestinal bleeding, splenic hemangiomas and left inferior vena cava  [cached]
Zhen-Kai Wang, Fang-Yu Wang, Ren-Min Zhu, Jiong Liu
World Journal of Gastroenterology , 2010,
Abstract: Klippel-Trenaunay syndrome is a congenital vascular anomaly characterized by a triad of varicose veins, cutaneous capillary malformation, and hypertrophy of bone and (or) soft tissue. Gastrointestinal vascular malformations in Klippel-Trenaunay syndrome may present with gastrointestinal bleeding. The majority of patients with spleenic hemangiomatosis and/or left inferior vena cava are asymptomatic. We herein report a case admitted to the gastroenterology clinic with life-threatening hematochezia and symptomatic iron deficiency anemia. Due to the asymptomatic mild intermittent hematochezia, splenic hemangiomas and left inferior vena cava, the patient did not seek any help for gastrointestinal bleeding until his admittance to our department for evaluation of massive gastrointestinal bleeding. He was referred to angiography because of his serious pathogenetic condition and inefficiency of medical therapy. The method showed that hemostasis was successfully achieved in the hemorrhage site by embolism of corresponding vessels. Further endoscopy revealed vascular malformations starting from the stomach to the descending colon. On the other hand, computed tomography revealed splenic hemangiomas and left inferior vena cava. To the best of our knowledge, this is the first Klippel-Trenaunay syndrome case presenting with gastrointestinal bleeding, splenic hemangiomas and left inferior vena cava. The literature on the evaluation and management of this case is reviewed.
KLIPPEL-TRENAUNAY SYNDEROME A CASE REPORT
K. SHAMIMI
Acta Medica Iranica , 1986,
Abstract: The Klippel-Trenaunay syndrome, first reported in 1910, is a triad of cutaneous hemangioma, varicose veins, and soft tissue or bony hypertrophy. The varicosities are extensive involving the tributaries of the greater or lesser saphenous systems. Arteriogram are normal with no evidence of arteriovenous fistulas. Multiple ligation and stripping may worsen the condition, and treatment consists of wearing elastic supporting hose. A similar condition but associated with arteriovenous fistula is known as the Parkes Weber syndrome.
Sturge Weber Syndrome Overlapping with Klippel Trenaunay Syndrome  [PDF]
Shatanik Sarkar,Chaitali Patra,Chandrasekhar Dey,Malay Kumar Dasgupta,Tapan Kumar Kundu
Journal of Nepal Paediatric Society , 2013, DOI: 10.3126/jnps.v33i2.7704
Abstract: Sturge Weber syndrome (SWS) is a mesodermal phakomatosis characterized by meningo-facial angiomas with cerebral calcification. Klippel Trenaunay syndrome (KTS) is another very rare type of phakomatosis with cutaneous angiomas, varicose veins and enlargement of soft tissue or bones. Overlap between SWS & KTS is very rarely encountered. We report a three and half year old girl with overlapping features of both SWS and KTS. DOI: http://dx.doi.org/10.3126/jnps.v33i2.7704 J Nepal Paediatr Soc. 2013; 33(2):147-149
Klippel-trenaunay syndrome associated with pseudo - Kaposi′s sarcoma
Irene N,Hema O,Rajagopalan V,Parveen B
Indian Journal of Dermatology, Venereology and Leprology , 2002,
Abstract: Pseudo Kaposi′s sarcoma is a rare vascular lesion, usually associated with arterio venous malformations oft he Parker Weber type, and only occasionally with Klippel Trenaunay syndrome per se. We report one such case.
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