Klippel-Trenaunay Syndrome (KTS) is a rare triad of congenital vascular
malformations involving extensive Port wine stains, soft tissue or bone
hypertrophy and underlying venous and/or lymphatic malformation affecting limb,
pelvicor abdominal organs. Pregnancy is known to exacerbate KTS complications
and can put women at increased obstetrical risk due to deep venous thrombosis
and other thromboembolic events. We report a case of a pregnant woman with KTS
with the personal antecedent of two episodes of pulmonary thromboembolism.