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Erdheim-Chester Disease with Right Atrial Tumor and “Temporal Arteritis”

DOI: 10.4236/ojra.2012.23008, PP. 37-38

Keywords: Erdheim-Chester Disease, Temporal Arteritis, Giant Cell Arteritis

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Erdheim-Chester disease is an unusual syndrome characterized by non-Langerhans cell histiocytosis which can mimic rheumatologic diseases. We report a case of Erdheim-Chester masquerading as giant cell arteritis, which was success-fully managed with anakinra as anti IL-1 therapy.


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